Vascular SarcoidosisA Rare Cause of Pulmonary Hypertension
作者:
LEWIS SMITH,
JEFFRY LAWRENCE,
ANNA-LUISE KATZENSTEIN,
期刊:
The American Journal of the Medical Sciences
(OVID Available online 1983)
卷期:
Volume 285,
issue 1
页码: 38-44
ISSN:0002-9629
年代: 1983
出版商: OVID
关键词: Sarcoidosis;Pulmonary hypertension;Granulomatous vasculitis
数据来源: OVID
摘要:
Pulmonary hypertension is an uncommon complication of sarcoidosis and is usually related to the development of end-stage, interstitial fibrosis or honeycomb lung. We describe a patient with sarcoidosis who developed pulmonary hypertension in the absence of significant parenchymal fibrosis. The pulmonary hypertension in this case was caused by granulomatous destruction of arteries and veins, as documented by an open-lung biopsy and autopsy. Clinical features, including pulmonary function tests, are presented which suggested that end-stage interstitial lung disease was not causing the hypertension. Recognition of this complication of sarcoidosis is important if effective therapy is to be found.
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