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Protein C Deficiency Producing a Moyamoya-Like Intracranial Arterial Occlusion and Resultant Multiple Cerebral Infarctions

 

作者: Sameer Farah,   Madhavan Ravindran,   Jassim A. Hussein,   Shemsudin Shlokovich,  

 

期刊: Medical Principles and Practice  (Karger Available online 1996)
卷期: Volume 5, issue 1  

页码: 43-46

 

ISSN:1011-7571

 

年代: 1996

 

DOI:10.1159/000157380

 

出版商: S. Karger AG

 

关键词: Protein C deficiency;Moyamoya disease;Multiple cerebral infarcts

 

数据来源: Karger

 

摘要:

A 20-year-old female with protein C deficiency presented with a vaso-occlusive disorder, producing multiple cerebral infarcts and a clinical picture of pseudobulbar palsy with tetraparesis. Cerebral angiography showed a moyamoya-like appearance. Anticoagulation stabilized her condition with no further clinical deterioration.

 

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