Protein C Deficiency Producing a Moyamoya-Like Intracranial Arterial Occlusion and Resultant Multiple Cerebral Infarctions
作者:
Sameer Farah,
Madhavan Ravindran,
Jassim A. Hussein,
Shemsudin Shlokovich,
期刊:
Medical Principles and Practice
(Karger Available online 1996)
卷期:
Volume 5,
issue 1
页码: 43-46
ISSN:1011-7571
年代: 1996
DOI:10.1159/000157380
出版商: S. Karger AG
关键词: Protein C deficiency;Moyamoya disease;Multiple cerebral infarcts
数据来源: Karger
摘要:
A 20-year-old female with protein C deficiency presented with a vaso-occlusive disorder, producing multiple cerebral infarcts and a clinical picture of pseudobulbar palsy with tetraparesis. Cerebral angiography showed a moyamoya-like appearance. Anticoagulation stabilized her condition with no further clinical deterioration.
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