Spinal Abnormalities in Camptomelic Dysplasia
作者:
Michael Coscia,
George Bassett,
J. Bowen,
James Ogilvie,
Robert Winter,
Susan Simonton,
期刊:
Journal of Pediatric Orthopaedics
(OVID Available online 1989)
卷期:
Volume 9,
issue 1
页码: 6-14
ISSN:0271-6798
年代: 1989
出版商: OVID
关键词: Camptomelic dysplasia;Dwarfism;Spinal deformity
数据来源: OVID
摘要:
Significant spinal abnormalities were found in eight patients (average age of 6 years, 5 months) with camptomelic dysplasia. The late ossification of the midthoracic pedicles served as a clear diagnostic criterion for the syndrome. Scoliosis averaging 63° was found in all seven nonquadriplegic cases. Thoracic hyperkyphosis averaging 126° was seen in six (75%) of the patients, while cervical kyphosis averaging 66° was noted in three (38%). Vertebral body hypoplasia appeared to be a major cause of deformity. This study clarifies that patients with camptomelic dysplasia are surviving longer than previously expected and therefore should have their spinal deformities treated aggressively.
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