PurposeIdiopathic congenital retraction of the lower eyelid is rare. To further define the clinical features of this condition, we describe two new cases.MethodsRetrospective chart review.ResultsIn both cases, eye movements were restricted ipsilaterally and the condition was nonprogressive. CT scans showed mildly enlarged inferior and medial rectus muscles in one patient and normal muscles in the other. All other orbital structures were normal.ConclusionsNo definite cause for the lower eyelid retraction could be found, but it appeared to be related to a tight inferior rectus muscle. These patients may represent a variant of ocular fibrosis syndrome.