SummaryThe analysis of the ocular manifestations encountered in some inherited disorders of metabolism demonstrated their frequency and diagnostic values in this type of diseases. The inborn errors of metabolism analyzed are : cystinosis. Wilson, Hurler and Fabry diseases, galactosemia, haemocystnuria. alcaptonuria, albinism, familial amaurotic idiocy, Niemann-Pick disease, metachromatic leuco-dystrophy and Farber disease.