首页   按字顺浏览 期刊浏览 卷期浏览 Focal Glomerular Sclerosis and Nephrotic Syndrome in Spondyloepiphyseal Dysplasia
Focal Glomerular Sclerosis and Nephrotic Syndrome in Spondyloepiphyseal Dysplasia

 

作者: Radovan Bogdanović,   Pravdoljub Komar,   Angelina Cvorić,   Vesna Nikolić,   Miodrag Sinotić,   Dragan Zdravković,   Miloš Ognjanović,   Mario Abinun,  

 

期刊: Nephron  （Karger Available online 1994）
卷期: Volume 66, issue 2  

页码: 219-224

 

ISSN:1660-8151

 

年代: 1994

 

DOI:10.1159/000187804

 

出版商: S. Karger AG

 

关键词: Focal glomerular sclerosis;Nephrotic syndrome;Spondyloepiphyseal dysplasia

 

数据来源: Karger

 

摘要:

The association of a spondyloepiphyseal dysplasia and disproportionate short stature with focal glomerular sclerosis is reported in two girls. Renal disease manifested by proteinuria at the age of 2.5 and 11 years, leading to treatment-resistant nephrotic syndrome over 15 and 45 months, respectively. One patient went into end-stage renal failure shortly after nephrotic syndrome developed, the other died from sepsis. The association of spondyloepiphyseal dysplasia and focal glomerular sclerosis with nephrotic syndrome may represent a distinct disease entity.

 

点击下载:  PDF (1006KB)



返 回