Background: Müllerian anomalies are associated with several gynecologic complications including endometriosis, infertility, and pelvic pain.Case: A woman with duplicate cervix and a non-communicating longitudinal vaginal septum, but no other uterine anomalies, presented with pelvic pain, secondary infertility, and a long history of endometriosis. She was treated with operative laparoscopy and excision of the vaginal septum.Conclusion: A thorough evaluation, including history, physical examination, and appropriate imaging techniques (hysterosalpingography and magnetic resonance imaging) facilitates accurate diagnosis of anatomical defects and any associated disease in cases of unusual mullerian anomalies. An accurate preoperative diagnosis allows a planned, efficient surgical approach.