&NA;Primary neoplasms of the choroid plexus in children are surgically treatable, and the encouraging results of surgical removal, even for carcinoma, justify an aggressive surgical approach, Forty cases operated on over a span of 45 years have been reviewed in detail, including a rereading of all microscopic slides. The prognosis for children with papilloma has been excellent. The 5‐year survival rate for children with carcinoma of the choroid plexus was 50%, and all deaths occurred within 7 months of operation. The patients whose carcinomas were totally removed had a better prognosis than did those with subtotal removal. (Neurosurgery25:327‐335, 1989)