Because color vision impairment is a loss of visual function that accompanies most ocular disease, information about the color sense provides vital data for use in clinical investigation and diagnosis. However, not all types of clinical tests of color vision arc equally applicable to the detection and evaluation of such acquired dyschromatopsias: in particular, pseudoisochromatic tables prove inadequate and inefficient when compared with sorting tests. In this study, twelve patients with Dominantly Inherited Juvenile Optic Atrophy were investigated with the following tests of color vision—the Ishihara, AOHRR and Farnsworth tritan (F2) pseudoisochromatic plates, the Farnsworth-Munsell 100 hue and 28 hue, the Panel D-15. and the Nagel Anomaloscope. Ten patients had an acquired dyschromatopsias: of these, eight had a tritan defect, one an achromasy and another a very mild unilateral chromatic amblyopia. As expected, the sorting tests proved superior to the pseudoisochromatic plates in the investigation. The way in which previous failure to test color vision properly delayed accurate diagnosis of the patients' condition is illustrated by reference to their ocular histories.