Foveal Cone Dysfunction Syndrome
作者:
Martin ten Hove,
R. Siatkowski,
J. Smith,
期刊:
Journal of Neuro-Ophthalmology
(OVID Available online 1998)
卷期:
Volume 18,
issue 1
页码: 9-14
ISSN:1070-8022
年代: 1998
出版商: OVID
关键词: Foveal cone;Photoreceptor disorders.
数据来源: OVID
摘要:
Our objective was to describe and expand the clinical spectrum of a rarely detected, previously reported photoreceptor disorder restricted to the foveal cones. Three patients with bilaterally decreased acuity and hemeralopia were examined to exclude a structural, vascular, inflammatory, or degenerative process. Each patient underwent a full neuroophthalmic examination, including full-field and focal cone electroretinogram (ERG). All three patients had normal-appearing fundi, mild dyschromatopsia, central or paracentral visual field depressions, normal full-field photopic and scotopic ERGs, and markedly reduced focal, foveal cone ERG responses. One patient had a ring scotoma and an asymptomatic family member with abnormal full-field and focal cone ERG. The syndrome of acquired foveal cone dysfunction presents as a bilateral, painless, progressive central visual loss with minimal or absent fundus changes. It eludes diagnosis until focal, foveal cone ERG is performed.
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