Biclonal Sézary Syndrome with Capillary Leak Syndrome
作者:
O. Dereure,
P. Portales,
J. Clot,
J.J. Guilhou,
期刊:
Dermatology
(Karger Available online 1994)
卷期:
Volume 188,
issue 2
页码: 152-156
ISSN:1018-8665
年代: 1994
DOI:10.1159/000247123
出版商: S. Karger AG
关键词: Sézary syndrome;Biclonality;Capillary leak syndrome
数据来源: Karger
摘要:
Sézary syndrome is a rare, usually monoclonal proliferation of T lymphoid cells. We report a case of this form of cutaneous T cell lymphoma with highly probable biclonality of neoplastic proliferation. Biclonality in malignant lymphoma is a rare feature, until now generally reported in B cell lymphoma. Its identification by accurate immunological studies could be of importance since one of the two populations can exhibit a less differentiated phenotype requiring a more aggressive therapeutic regimen than usual. The occurrence of anasarca in our patient was probably due to capillary leak syndrome, already discussed in another case of peripheral T cell lymphoma
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