摘要:

We have evaluated the effect of oral administration of arginine chlorhydrate on the growth hormone response to growth hormone releasing hormone in a group of nine short prepubertal children (six boys and four girls). Arginine chlorhydrate 10 g, administered orally 60 min before an iv bolus injection of growth hormone releasing hormone 1–29, 1 μg/kg, significantly enhanced the growth hormone response to the neuropeptidc, confirming the results of previous studies which used the iv route. Furthermore, our data strengthen the view that the effects of arginine chlorhydrate on growth hormone secretion are mediated by inhibition of endogenous somatostatin relea

ISSN:0803-5253    

DOI:10.1111/j.1651-2227.1993.tb12586.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY

摘要:

Hallucinations on withdrawal of midazolam have been noted in intensive care patients. Isoflurane is increasingly used as an alternative drug for sedation. We report a scven‐year‐old child with 15% burns who, on withdrawal of isoflurane, suffered hallucinations, a generalized seizure and disorientation. The adverse symptoms occurred within hours of stopping the isoflurane and lasted for five d

ISSN:0803-5253    

DOI:10.1111/j.1651-2227.1993.tb12587.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY

摘要:

Small bowel biopsy in a 4–year‐old girl with symptoms suggestive of coeliac disease revealed subtotal villous atrophy. The mucosa healed on a gluten‐free diet. From the age of 7 years, the girl was challenged with gluten. Annual biopsies showed normal or nearly normal mucosa specimens. At 21 years of age, after 14 years of gluten challenge, a mucosal relapse was found and a gluten‐free diet was reinstituted. A biopsy one year later showed a normal mucosa. From this case report it is apparent that a patient with a past history of subtotal villous atrophy, which after a preceding period of gluten‐free diet does not recur within two years of gluten challenge, must be followed carefully, so as not to miss a lat

ISSN:0803-5253    

DOI:10.1111/j.1651-2227.1993.tb12588.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY

摘要:

An unusual case of cholelithiasis in an 18–month‐old boy with cervico‐oculo‐acoustic (Wildervanck's) syndrome is presented. Our patient had Duane's retraction syndrome, Klippel‐Feil anomaly and congenital deafness. To our knowledge this is the first case in which a probable association between cholelithiasis and Wildervanck's syndrome has been recorded. On the other hand, the presence of mutual malformations and anomalies such as scoliosis, ventricular septal defect, ectopic kidney, hydrocephalus, hypoplastic thumb and growth retardation seems to suggest that Wildervanck's syndrome is a clinical variant of Klippel‐Fe

ISSN:0803-5253    

DOI:10.1111/j.1651-2227.1993.tb12589.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY

摘要:

Lipoid proteinosis (Urbach‐Wicthe disease) is a rare autosomal recessive disorder in which hyalinized material is deposited in the skin, mucous membranes and brain. Laryngeal changes resulting in hoarseness may be present at birth or in early infancy, often being the first sign of the discase. A typical case is presente

ISSN:0803-5253    

DOI:10.1111/j.1651-2227.1993.tb12590.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY

ISSN:0803-5253    

DOI:10.1111/j.1651-2227.1993.tb12591.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY

ISSN:0803-5253    

DOI:10.1111/j.1651-2227.1993.tb12592.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY

ISSN:0803-5253    

DOI:10.1111/j.1651-2227.1993.tb12593.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY

ISSN:0803-5253    

DOI:10.1111/j.1651-2227.1993.tb12594.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY

ISSN:0803-5253    

DOI:10.1111/j.1651-2227.1993.tb12595.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY