摘要:

We reviewed the autopsy, clinical, and radiographic records of 39 patients with metastatic skeletal disease (age range 18 months-20 years). There were 11 different primary tumors responsible for skeletal metastases, of which neuroblastoma was the most common (16 patients). Other commonly occurring tumors giving rise to secondary skeletal deposits were rhabdomyosarcoma (seven), teratoma-teratocarcinoma (four), and Wilms tumor (three). Overall patient survival ranged from 2 weeks to 72 months, with an average of 10.2 months. Those patients presenting without skeletal metastases at the time of diagnosis of the primary tumor had a survival time averaging 16.2 months (range 3–72 months), whereas those patients presenting initially with skeletal metastases at the time of diagnosis of the primary tumor had a survival time of 8.5 months (range 0.5–23 months).

ISSN:0271-6798    

出版商:OVID    

年代:1985

数据来源: OVID

摘要:

Two children with rhabdomyosarcoma who developed slipped capital femoral epiphyses following pelvic irradiation are described. Previous case reports are summarised, and the relevant orthopedic implications of the disorder discussed.

ISSN:0271-6798    

出版商:OVID    

年代:1985

数据来源: OVID

摘要:

Sixty-one sequential patients initially referred because of hand-reduction abnormalities were retrospectively reviewed. Twenty distinct diagnoses were recognized. Particularly noteworthy was the number of instances in which standard classification schemes failed to explain fully the structural or syndromic characteristics in this group of patients. One-fourth (15 of 61) of the diagnoses were of disorders resulting from abnormalities of single genes; more than one-third (21 of 61) had multiple malformation syndromes. The importance of dysmorphologic and genetic investigation of individuals with congenital reduction malformations of the hands is evident from these data and from the cases presented.

ISSN:0271-6798    

出版商:OVID    

年代:1985

数据来源: OVID

摘要:

Arthrogryposis multiplex congenita is a rare congenital disorder in which the extremities are affected with severe resistant musculoskeletal contractures. In the upper extremity, these deformities typically consist of internal rotational contractures of the shoulder, extension deformity of the elbow, flexion and ulnar deviation of the wrist, thumb-in-palm deformity, and digital interphalangeal joint flexion contractures occurring singularly or in combination. At the Houston Unit of the Shriners Hospital for Crippled Children, during the interval from 1962 to 1982, 25 patients underwent 56 operative procedures to correct upper-extremity deformities due to arthrogryposis multiplex congenita. Functional improvement was observed clinically and reported subjectively by the patients or their parents in 75% of the cases.

ISSN:0271-6798    

出版商:OVID    

年代:1985

数据来源: OVID

摘要:

Four patients with weak triceps muscle function, secondary to obstetrical palsy, were treated by transfer of the latissimus dorsi on its neurovascular pedicle to provide effective elbow extension. The average age of the patients at surgery was 10 years, and follow-up ranged from 12 to 53 months. Postoperatively, all patients demonstrated increased strength of elbow extension and improvement in activities of daily living. These satisfactory results support the use of latissimus dorsi transfer in patients with weak elbow extension secondary to obstetrical palsy.

ISSN:0271-6798    

出版商:OVID    

年代:1985

数据来源: OVID

摘要:

Two cases of partial defects of the ulna in the growing child were successfully treated with the one-bone forearm procedure and followed up for 1 and 5 years, respectively. Stable elbow and forearm could be established by synthesis of the proximal part of the ulna and the distal part of the radius. Cosmetic and functional improvement was achieved in spite of a limitation of pronation-supination in the forearm. Longitudinal growth of the affected forearm was maintained during the follow-up period after correction at surgery.

ISSN:0271-6798    

出版商:OVID    

年代:1985

数据来源: OVID

摘要:

A surgical technique for distal transverse osteotomy of the tibia and fibula to correct torsional malalignment of the leg is described. Thirty-two derotation osteotomies have been performed on 19 patients, whose average age at the time of surgery was 12 years; average follow-up was 2 years. Average torsional change following surgery was 38. Ninety-four percent of the patients available for follow-up (16 of 17) had a successful outcome. The two small incisions required in this procedure are cosmetically acceptable, and the location of the osteotomy in metaphyseal bone provides stability. We conclude that this osteotomy is a simple, safe, and effective procedure for correction of torsional malalignment in carefully selected patients.

ISSN:0271-6798    

出版商:OVID    

年代:1985

数据来源: OVID

摘要:

Observations on the size of the femoral head in congenital dislocation of the hip are presented. The long-term effects of open reduction and innominate osteotomy on the size of the femoral head are assessed. Innominate osteotomy does not cause overgrowth of the femoral head, although open reduction results in mild coxa magna. The pathophysiology and significance of coxa magna are discussed.

ISSN:0271-6798    

出版商:OVID    

年代:1985

数据来源: OVID

摘要:

Eighteen unrelated children (12 boys and six girls) with Osgood-Schlatter disease (OSD) were evaluated by history, physical examination, and histocompatibility antigen [human leukocyte antigen (HLA)] determination. Four boys and two girls had pain at sites other than the tibial tuberosity. By history, other related individuals with a diagnosis of OSD were found in six of the 18 families. The distributions of HLA antigens (A, B, andDR) were not demonstrably abnormal. The similarity of OSD and enthesitis accompanying HLA-B27-associated arthropathy may cause diagnostic difficulty. The lack of an association between OSD and HLA-B27 may be of assistance in differentiating the two disorders.

ISSN:0271-6798    

出版商:OVID    

年代:1985

数据来源: OVID

摘要:

We had the opportunity to examine a naturally occurring Salter-Harris Type I fracture in the distal tibia of a 9-year-old boy. The injury was simultaneous with traumatic amputation of the extremity a few centimeters distal to the knee. The epiphyseal plate was examined microscopically, and the plane of cleavage was found not to be uniform, but to involve the zones of resting, proliferating, hypertrophying, and provisionally calcified cartilage cells. We hope by demonstrating the inconsistency of the cleavage plane in this case to assist in understanding the complexity of physeal fractures and the unpredictable results that occasionally occur.

ISSN:0271-6798    

出版商:OVID    

年代:1985

数据来源: OVID