摘要:

SYNOPSISA study has been made of the foetal outcome in 38 pregnancies complicated by maternal autoimmune disease over a 10 year period at a Sydney hospital. The diseases included thyrotoxicosis, idiopathic thrombocytopaenic purpura, myasthenia gravis, systemic lupus erythematosus and scleroderma. The occurrence of perinatal manifestations of these maternal disorders is of importance both in the paediatric management of such cases and in the study of aetiological factors in autoimmune disease.

ISSN:1034-4810    

DOI:10.1111/j.1440-1754.1972.tb01843.x

出版商:Blackwell Publishing Ltd    

年代:1972

数据来源: WILEY

摘要:

SYNOPSISThis survey comprises a retrospective analysis of 132 cases of idiopathic thrombocytopenic purpura (ITP) treated at the Royal Children's Hospital from 1958 to 1966 inclusive.There was a high spontaneous remission rate in this disease in children. A comparison of the results of treatment with and without steroids suggests that steroids initially help to control the bleeding tendency and in some cases a temporary elevation in platelet count follows their use. However in the two groups there was no difference in the long‐term remission rate or in the remission time.While only about half the splenectomized patients have achieved full remission with a normal platelet count, they were all symptomless without the use of long‐term stero

ISSN:1034-4810    

DOI:10.1111/j.1440-1754.1972.tb01844.x

出版商:Blackwell Publishing Ltd    

年代:1972

数据来源: WILEY

摘要:

SYNOPSIS8 mentally retarded but otherwise healthy phenylketonuric individuals were given two oral loads of phenylalanine (100 mgm/Kg). One of these loads was accompanied by β‐2‐thienylalanine (20 mgm/Kg). Blood levels of phenylalanine in the 6 hours after the two phenylalanine loads were compared. β‐2‐thienylalanine reduced the levels of phenylalanine in every case.This suggests that if the phenylketonuric child were to take an appropriate amount of β‐thienylalanine with meals, he might be able to eat more phenylalanine, and this would allow a considerably more liberal diet.As diet has been shown to be a dominant factor in the emotional climate of families of phenylketonuric children, this stress would be considerably reduced. Thus, the administration of β‐thienylalanine might lead to a more normal social development

ISSN:1034-4810    

DOI:10.1111/j.1440-1754.1972.tb01845.x

出版商:Blackwell Publishing Ltd    

年代:1972

数据来源: WILEY

ISSN:1034-4810    

DOI:10.1111/j.1440-1754.1972.tb01846.x

出版商:Blackwell Publishing Ltd    

年代:1972

数据来源: WILEY

摘要:

SYNOPSISA technique for studying skeletal disorders by using stable strontium as a tracer for calcium is described. Patients with nutritional and hypophosphataemic vitamin resistant rickets, with osteoporosis and osteogenesis imperfecta, and with osteopetrosis have been studied. Results are correlated with other tests, particularly calcium infusion, calcium balance, bone biopsy and response to calcitonin. The test has proved helpful in delineating two distinct types of osteoporosis, and has provided further evidence for a primary bone defect in one child with vitamin resistant rickets.

ISSN:1034-4810    

DOI:10.1111/j.1440-1754.1972.tb01847.x

出版商:Blackwell Publishing Ltd    

年代:1972

数据来源: WILEY

摘要:

SYNOPSISA case of 7 year old Danish girl with spondylo‐metaphyseal dysplasia is reported. The disease is characterised clinically by shortening of stature and thoracic kyphosis. The radiographic pattern of the vertebral column, metaphyses and round bones of the hands and feet, is diagnostic in this syndrome. Degenerative bone changes supervene early in adult lif

ISSN:1034-4810    

DOI:10.1111/j.1440-1754.1972.tb01848.x

出版商:Blackwell Publishing Ltd    

年代:1972

数据来源: WILEY

摘要:

SYNOPSISA case of a 5 year old Polish girl with Dyggve disease is reported. The radiographic pattern of the vertebral column and pelvis is diagnostic in this syndrome. The course of the disease in infancy and in adult life is at present unknown.

ISSN:1034-4810    

DOI:10.1111/j.1440-1754.1972.tb01849.x

出版商:Blackwell Publishing Ltd    

年代:1972

数据来源: WILEY

摘要:

SYNOPSISThis is a report of a rare, very malignant ovarian tumour occurring in a 12 year old Italian girl.An aggressive approach was adopted which included excision of the primary tumour under cover of chemotherapy, followed by a second exploratory laparotomy, and excision of a single pulmonary metastasis.

ISSN:1034-4810    

DOI:10.1111/j.1440-1754.1972.tb01850.x

出版商:Blackwell Publishing Ltd    

年代:1972

数据来源: WILEY

摘要:

Book reviewed in this article:An Introduction to Diabetes for the Young Child. Written and illustrated by Mary Pinckney Ferguson, Charles C. Thomas, Publisher Springfield, Illinois, U.S.A. 1972.The Prevention of Perinatal Morbidity and Mortality, Report on a seminar, Geneva, 1971 (Public Health Papers, No. 42)The Pathophysiology and Treatment of Drowning and Near‐Drowning by Jerome H. Modell. Published by Charles C. Thomas, Springfield, Illinois, 1971.The treatment of the child at home. A guide for Family Doctors, by R. S. IllingworthThe Autistic Syndrome. Proceedings of a Working Party, University of Queensland, August, 1969. Edited by John Rendle‐Short and Helen Clancy, Faculty of Medicine.Your Child has Diabetes. John M. Court.The Normal Child. R. W. Illingwo

ISSN:1034-4810    

DOI:10.1111/j.1440-1754.1972.tb01851.x

出版商:Blackwell Publishing Ltd    

年代:1972

数据来源: WILEY