摘要:

Abstract:We attempted to estimate the level of Greek mothers' knowledge relating to the harmful effects of sunlight and whether this knowledge led to protective measures for them and their children. Between September and November 1993, 315 mothers were randomly selected from the outpatient department of our hospital and interviewed by questionnaire about themselves and their children (56% boys, 44% girls, ages 1–12 yrs). Knowledge was estimated by an index score that for 28% of the mothers was considered poor, for 50% moderate, for 16% good, and for only 6% very good or excellent. The score was positively associated with parent education, urban residence, mother's job relevant to the cosmetics industry or the mass media, and history of sunburn in one or both parents. Scores were also established for sunlight‐protective measures taken for themselves (28% poor, 45% moderate, 27% just good) and for their children (24% poor, 46% moderate, 30% just good). These scores were significantly associated only with mothers' knowledge of sun protection. Mothers who used sun protection for themselves also applied it to their children. This study shows that mothers in Greece should be encouraged both to increase their knowledge of sun protection and steadily incorporate it into their knowledge of sun protection and steadily incorporate it into their lifest

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1995.tb00159.x

出版商:Blackwell Publishing Ltd    

年代:1995

数据来源: WILEY

摘要:

Abstract:Infantile acropustulosis is a recurrent, pruriginous, vesiculopustular eruption of the palms and soles first described in 1979. We report six cases of infantile acropustulosis in recently emigrated children treated for scabies. Clinical follow‐up was obtained by questionnaire addressed to patients'families and general practitioners. Our study suggests infantile acropustulosis is frequent in immigrant infants and could be a non‐specific hypersensitivity reaction to Sarcoptes scab

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1995.tb00160.x

出版商:Blackwell Publishing Ltd    

年代:1995

数据来源: WILEY

摘要:

Abstract:Generalized anhldrosls with heat collapse, painful fingers, and angiokeratomas were the presenting signs in a 23‐year‐old man who was shown by enzyme studies and electron microscopy to have Fabry disease. His 6‐year‐old brother had the early diagnostic findings of episodic painful fingers, heat intolerance, and retroaurlcular telangiectasia. Both had an absence of α‐galactosidase, Over 6 years of observation, the older brother developed progressive renal failure and the younger one developed acrodynla and anhidrosls. Their mother had dlminished α‐galactosidase activity and several anglomatous papules on one breast A review of Fabry disease emphasizes the need for skin Inspection for anglomas and telanglectasia, and enzyme assay in patlents with lnexplicable complaints or lindings. Carrier females are most easily recognized by the presence of unique com

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1995.tb00161.x

出版商:Blackwell Publishing Ltd    

年代:1995

数据来源: WILEY

摘要:

Abstract:The prevalence of persistent microalbumlnuria, retinopathy, and peripheral and autonomic neuropathy was assessed In 18 children and adolescents with type 1 (insulin‐dependent) dlabetes mellitus (IDDM) who suffered from necrobiosls llpoldlca diabeticorum (NLD) and in 40 dlabetics without NLD, matched for sex, age, duration of disease, and metabolic control. The mean ± SD age ot the patients was 15.1 ± 8.6 years (range 7.9–23.9 yrs) and their duration of IDDM was 10.9 ± 8.1 years (range 7.1–21.0 yrs). Their mean glycosylated hemoglobin level was 9.9 ± 5.0% (7.3–16.6%) and their fructosamine level was 274 ± 180 μmol/L (199–466 μmol/L). Patients with NLD had a higher frequency of persistent microalbumlnuria (p<0.001) and retlnopathy (p<0.001) than those without NLD. Our study suggests that children as well as adult diabetics with NLD can be at high risk for nephropathy and retinopathy; NLD can be a clue for diabetic nephropathy

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1995.tb00162.x

出版商:Blackwell Publishing Ltd    

年代:1995

数据来源: WILEY

摘要:

Abstract:Infantile acute hemorrhagic edema (IAHE) is a leukocytoclastic vasculitis that is contined to the skin without visceral Involvement. Edema and purpuric lesions characterize the disease. The disorder has a dramatic onset, with a short, benign course and spontaneous resolution within several weeks. The clinical similarities between IAHE and Henoch‐Shünlein purpura have been discussed in the literature. We report three Infants with IAHE and discuss the clinical, laboratory, and histopathologic features of the disease. We suggest that it should be regarded as a separate entity for appropriate diagnostic investigations and thera

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1995.tb00163.x

出版商:Blackwell Publishing Ltd    

年代:1995

数据来源: WILEY

摘要:

Abstract:Aplasia cutis congenita is a rare disorder characterized by localized absence of skin at birth. Type V in Frieden's classification, which is associated with fetus papyraceous or placental infarcts, occurs as a large cutaneous defect on the trunk and extremities. The patient we report had a lesion affecting the trunk and extremities symmetrically, with no family history of the disorder or chromosomal abnormalities. In our opinion, despite the absence of fetus papyraceous or placental infarct, this patient's condition can be classified as type V.

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1995.tb00164.x

出版商:Blackwell Publishing Ltd    

年代:1995

数据来源: WILEY

摘要:

Abstract:A 4‐year‐old girl was seen in our department for erythroderma, palmoplantar hyperkeratosis, and scalp desquamation present since birth. The dermatosis had run an intermittent course, with exacerbations after Infections and spontaneous remissions. A specimen from a skin biopsy performed at 1 year of age showed the characteristic features of psoriasis, findings that were confirmed in our biopsy specimen. Treatment with acltretin controlled the outbreaks. At 7 years of age she has developed, for the first time, plaque type psoriasis. Congenital erythroderma is an unusual form of psoriasis with a wide differential diagno

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1995.tb00165.x

出版商:Blackwell Publishing Ltd    

年代:1995

数据来源: WILEY

摘要:

Abstract:Immunodeficiency with hyperlmmunoglobullnemia M is a rare disease characterized by very low levels of IgG and IgA and normal or high levels of serum IgM and IgD. Recurrent and severe systemic infections with pathogenic bacteria are frequent if immunoglobulin replacement therapy is not given. Histoplasmosis is a systemic granulomatous mycosis due to Histoplasma capsutatum and characterized by a particular affinlty for the reticuloendothellal system. Glabrous skin involvement in histoplasmosis is highly unusual except in patients with advanced human Immunodeficiency viral disease. Cutaneous histoplasmosis and granulomatous reaction were diagnosed in a 5‐year‐old boy with hype‐IgM disease. The lesion Improved after oral ketoconazole therapy. To our knowledge, this is the first case of cutaneous histoplasmosis associated with hype‐IgM to be r

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1995.tb00166.x

出版商:Blackwell Publishing Ltd    

年代:1995

数据来源: WILEY

摘要:

Abstract:We report the second infant of nonconsanguineous parents with epidermolysis bullosa junctionalls associated with urinary bladder extrophy, epispadias, anterlorized anus, and bilateral inguinal hernias. The family history also included the death of a maternal cousin due to epidermolysis bullosa. Our diagnosis was based on electron microscopy and immunofluorescence evidence. This patient is reported because of the rarity of this constallation of findings.

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1995.tb00167.x

出版商:Blackwell Publishing Ltd    

年代:1995

数据来源: WILEY

摘要:

Abstract:Glomangiomas, or multiple glomus tumors, occur in disseminated, localized, or congenital plaquelike forms. The first two cases of congenital plaquelike glomangioma were described in 1990. We report a 9‐year‐old girl with a congenital, violaceous, 75‐cm2indurated plaque of the left abdomen that showed the classic histologic findings of glomangioma. In our review of the world literature, we found 11 additional, welldocumented cases of glomangioma present at birth. Ten of these patients had violaceous indurated plaques, and the other two had clusters of discrete nodules. The majority of lesions were painless and enlarged with body growth. Many patients developed satellite lesions at sites distant from the original glomangiomas later in life. Family history of glomangioma was positive in 4 of the 12 pat

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1995.tb00168.x

出版商:Blackwell Publishing Ltd    

年代:1995

数据来源: WILEY