摘要:

In an attempt to visualize the pulmonary arterial trees of neonates and infants with ductus‐dependent decreased pulmonary flow, the efficacy of retrograde injection of contrast from the radial arteries of 11 consecutive patients was tested. All patients had pulmonary atresia and patent ductus arteriosus. A 22‐ or 24‐gauge needle was inserted into the radial artery and contrast medium of 2 ml/kg was injected at flow rates of 3 to 4 ml/sec. The pulmonary arteries were filled by retrograde flow through the ductus arteriosus. This method provided clear visualization of the pulmonary arteries, especially by ductus‐sided injections. Developmental anomalies of the pulmonary trunk, localized stenosis at the ductus, and aortopulmonary collateral arteries were demonstrated. No complications occurred during angiography, and all the procedures were completed within 30 minutes. This method appears to be useful in detecting anatomical abnormalities of the pulmonary arteries in neonates and infants with ductus‐dependent decreased pulmo

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1992.tb00926.x

出版商:Blackwell Publishing Ltd    

年代:1992

数据来源: WILEY

摘要:

We here report a unique case of a young boy with an intrathoracic tumor which consisted of neurogenic and myogenic elements. The initial pathological diagnosis was alveolar rhabdomyosarcoma. The tumor tissue from surgical resection was composed of three parts, each showing a different histological appearance, i.e. a monotonous small cell area, an alveolar area, and an area consisting of pleomorphic rhabdomyoblasts. The small round cells in the monotonous area were immunoreactive with the antibodies for Leu7, neuron‐specific enolase (NSE), neurofilament proteins (NFP), and β2microglobulin, but not with the antibody for desmin. These cells also had dense core granules. The tumor cells in the alveolar area were immunoreactive with the antibodies for Leu7 and desmin, but not with the antibody for NFP. Pleomorphic rhabdomyoblasts were immunoreactive with the antibody for desmin, but not with the antibodies for Leu7 and NFP. These findings imply that this tumor consisted of neurogenic and myogenic elements and is considered to be a special type of rhabdomyosarco

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1992.tb00927.x

出版商:Blackwell Publishing Ltd    

年代:1992

数据来源: WILEY

摘要:

We report a case of Farber disease (Farber lipogranulomatosis). The main features were a shrill voice, joint swelling, subcutaneous nodules and retarded psychomotor development. Cytological investigation revealed intracytoplasmic inclusion bodies characteristic of Farber disease. Lipid analysis of liver tissue indicated an accumulation of ceramide containing non‐hydroxy fatty acids. It was found that the acid ceramidase activity in the liver was reduced to 31% of the control value. In this patient there were also persistent diarrhea, cholelithiasis, transient proteinuria and increased urinary total sialic acids. These features have not been noted in previously reported case

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1992.tb00928.x

出版商:Blackwell Publishing Ltd    

年代:1992

数据来源: WILEY

摘要:

A five year old girl with cardiac tamponade due to purulent pericarditis caused by Staphylococcus aureus was treated successfully with a combination therapy of appropriate antibiotics and surgical open drainage. Right atrial collapse was observed during early systole using two‐dimensional echocardiography. This case illustrated the usefulness of echocardiography for early detection and treatment of cardiac tamponade in pediatric patient

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1992.tb00929.x

出版商:Blackwell Publishing Ltd    

年代:1992

数据来源: WILEY

摘要:

The pathogenesis and etiology of Kawasaki disease are unknown, but some studies suggest increased genetic susceptibility. The case is presented of an infant with Kawasaki disease whose father suffered from the same illness 21 years previously. The A, B and C loci of the HLA antigens were examined.

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1992.tb00930.x

出版商:Blackwell Publishing Ltd    

年代:1992

数据来源: WILEY

摘要:

A case of intestinal myiasis in an 8‐month‐old girl is reported. The clinical symptoms were ill humor and mucous bloody stools containing a number of moving worms, which were identified as second‐instar larvae of Sarcophaga pere

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1992.tb00931.x

出版商:Blackwell Publishing Ltd    

年代:1992

数据来源: WILEY

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1992.tb00932.x

出版商:Blackwell Publishing Ltd    

年代:1992

数据来源: WILEY

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1992.tb00933.x

出版商:Blackwell Publishing Ltd    

年代:1992

数据来源: WILEY

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1992.tb00934.x

出版商:Blackwell Publishing Ltd    

年代:1992

数据来源: WILEY

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1992.tb00935.x

出版商:Blackwell Publishing Ltd    

年代:1992

数据来源: WILEY