摘要:

Portal vein blood flow in healthy children was measured using a duplex ultrasound system consisting of a B mode linear scanner and a single Doppler transducer. Portal blood flow volume (PBFV) correlated with age, height, weight and body surface area. Increases in PBFV with age were greater in boys than girls. A correlation was noted between the diameter of the portal vein and PBFV (r=0.89). However, the maximum portal blood flow velocity (Vmax) did not correlate with age, height, weight or body surface area. Increases in PBFV in accordance with physical development was thought to depend mainly on widening of the portal vein and not on acceleration of portal blood flow velocity. The formula for calculating PBFV by multivaliate statistical analysis is as follows:PBFV(ml/min)=30.1×age(yrs)‐1.07×height(cm)=3.31×weight(kg).Portal vein flowmetry using a duplex ultrasound system may be useful for evaluation of the hepatic circulation in chil

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1991.tb02592.x

出版商:Blackwell Publishing Ltd    

年代:1991

数据来源: WILEY

摘要:

We describe 50 patients with suppurative regional lymphadenitis following intradermal BCG vaccination. For non‐drained suppurations we performed needle aspiration in twenty‐three patients (aspiration group). Of the remaining 27 patients (drainage group) 16 had spontaneous drainage and 11 incisional drainage. In the drainage group, 17 patients were followed up conservatively. Ten patients from the drainage group and 3 patients from the aspiration group (drained after needle aspiration) accepted total surgical excision to terminate the drainage. Twenty of twenty‐three patients in the aspiration group recovered after needle aspiration. Average period of cessation of drainage and healing of wound was 7.5 weeks in patients with drainage (spontaneous and incisional). Healing was complete after total surgical excision of draining suppurations in all of 11 patients. We concluded that simple needle aspiration was sufficient for the treatment of suppurating but non‐drained BCG lymphadenitis. For suppurating lymph nodes that were surgically (not recommended) or spontaneously drained, a more invasive procedure, total surgical excision, was proposed to terminate the long and disturbing drainage

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1991.tb02593.x

出版商:Blackwell Publishing Ltd    

年代:1991

数据来源: WILEY

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1991.tb02594.x

出版商:Blackwell Publishing Ltd    

年代:1991

数据来源: WILEY

摘要:

An association of human leukocyte antigens (HLA) with idiopathic nephrotic syndrome (INS) in childhood was studied to characterize the immunogenetic background. We determined the class I antigens using the microlymphocytotoxicity test as well as class II antigens (DRB, DQB, DQA) and class III antigen (complement 4) using DNA restriction fragment length polymorphism (RFLP) in 36 children with INS. In the current study, neither the single allele in HLA class I antigen nor the single gene frequency in the class II region was significantly increased, in contrast to the results in Caucasian INS patients in whom a genetic predisposition to the HLA system, especially to HLA B8, DR3, and DR7, has been frequently reported. Also, in our data, the frequency of deletion of complement 4 gene was not different from that of the controls. These data suggest that there is a difference in immunogenetic background between Caucasian and Japanese INS patients as far as HLA is concerned.

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1991.tb02595.x

出版商:Blackwell Publishing Ltd    

年代:1991

数据来源: WILEY

摘要:

Caroli's disease is a rare congenital anomaly of the liver. Since new diagnostic techniques for the evaluation of hepatic disease have been introduced, the number of reported cases of Caroli's disease has been gradually increasing. This report describes the case of a 13 year old girl with nausea, vomiting, fever and hepatomegaly. The diagnosis of Caroli's disease was established by ultrasonography and CT scan. The complications and management are discussed. The important points in management are to relieve symptoms and to conduct regular examinations by ultrasonography for the early detection of hepatobiliary carcinoma.

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1991.tb02596.x

出版商:Blackwell Publishing Ltd    

年代:1991

数据来源: WILEY

摘要:

A case of Prader‐Willi syndrome who later developed hepatoblastoma is reported. Prader‐Willi syndrome was suspected because of hypotonia, hypopigmentation, and undescended testes when he was a newborn infant. The diagnosis was confirmed by chromosome analysis, which showed 46XY del(15)(qll, ql3). When he was 1 year 4 months old, a liver tumor and high serum AFP were found. At operation a large tumor arising from the caudate lobe was found and the tumor was totally resected. After completion of the hepatectomy, he developed circulatory collapse of unknown cause and died shortly after the operation. Histopathologic examination revealed that the tumor was composed of two components, well differentiated cells and poorly differentiated cells. The well differentiated part did not dominate the poorly differentiated part, so it was diagnosed as poorly differentiated hepatoblastoma. This is the first reported case of Prader‐Willi syndrome with a pediatric malignant

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1991.tb02597.x

出版商:Blackwell Publishing Ltd    

年代:1991

数据来源: WILEY

摘要:

The case is presented of a four year old boy with a large left abdominal mass. The patient was diagnosed as having a left giant hydroureteronephrosis due to a primary obstructed megaureter, based on the findings of ultrasonography, micturating cystourethrography, excretion urography, computed tomography and percutaneous antegrade pyeloureterography. Diuretic renography showed that the obstruction was partial. Since a static renal scintigram indicated that renal function on the affected side was moderately well preserved, ureteroplasty is planned.

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1991.tb02598.x

出版商:Blackwell Publishing Ltd    

年代:1991

数据来源: WILEY

摘要:

Herein we report an infantile case of congenital hydrocolpos combined with left renal agenesis which presented with an abnormal mass protruding from the vaginal introitus. The diagnosis was made shortly after birth by ultrasonography and confirmed by other radiologic diagnostic methods. This case highlights the value of ultrasonography in diagnosing hydrocolpos and determining the coexistence of renal anomalies.

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1991.tb02599.x

出版商:Blackwell Publishing Ltd    

年代:1991

数据来源: WILEY

摘要:

We report two siblings with autoimmune neutropenia of infancy. Patient 1 was hospitalized for viral gastroenteritis at 5 months of age, when his absolute neutrophil count was 684/mm3. Absolute neutrophil counts ranging from 0 to 930/mm3continued but normalized spontaneously at 25 months of age. Patient 2, a younger brother of patient 1, had prolonged high grade fever at 5 months, when his absolute neutrophil count was 138/mm3. Absolute neutrophil counts ranging from 96 to 1,078/mm3continued for the following 9 months. Antineutrophil antibodies were detected in the patients' sera. Our cases are siblings and each case was independently affected, since the diagnoses were made at 5 months of age and the interval between the diagnoses was 23 months. Autoimmune neutropenia of infancy is comparatively rare, so that we think that the disease in these siblings was due to a genetic abnormality.

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1991.tb02600.x

出版商:Blackwell Publishing Ltd    

年代:1991

数据来源: WILEY

ISSN:1328-8067    

DOI:10.1111/j.1442-200X.1991.tb02601.x

出版商:Blackwell Publishing Ltd    

年代:1991

数据来源: WILEY