| 1. |
Kidney Glycolipids in Late Infantile Metachromatic Leucodystrophy |
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Acta Pædiatrica,
Volume 55,
Issue 1,
1966,
Page 1-9
ERIK MÅRTENSSON,
ALAN PERCY,
LARS SVENNERHOLM,
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摘要:
Summary1. Micropreparations from kidneys of children with metachromatic leucodystrophy were analyzed for neutral glyco‐lipid and sulfatide patterns.2. Sulfatides, neutral glycolipids, and He has supported his hypothesis by the isolation of a sulfatide sulfatase from kidney and by the demonstration of sulfatase activity in many other organs, including brain [7]. He has also presented evidence for a decreased activity of this enzyme in metachromatic leucodystrophy. The available data can then be interpreted according to the following scheme: gangliosides were isolated from a single case of metachromatic leucodystrophy and from a pooled sample of normal kidneys.3. The sulfatide content of the pathological material was increased 70‐fold over normal. The concentration of total neutral glycolipids and gangliosides were similar in normal and pathological material, but definite variations in the ganglioside TLC pattern were detected.4. Sulfatide fatty acid analyses differed from those of normal material. There was an increase of the hydroxy acids and of the normal C‐acids, and a decreased degree of unsaturation. Possible mechanisms for these changes are discussed.5. Metabolic pathways of sulfatides and cerebrosides are discussed in relation to the disease mech
ISSN:0803-5253
DOI:10.1111/j.1651-2227.1966.tb15202.x
出版商:Blackwell Publishing Ltd
年代:1966
数据来源: WILEY
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| 2. |
BRONCHIECTASIS: A REVIEW OF 187 CASES IN CHILDREN WITH FOLLOW‐UP PULMONARY FUNCTION STUDIES IN 58 |
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Acta Pædiatrica,
Volume 55,
Issue 1,
1966,
Page 3-16
ELINOR M. GLAUSER,
CHARLES D. COOK,
G. B.C. HARRIS,
J. H. SHAW,
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ISSN:0803-5253
DOI:10.1111/j.1651-2227.1966.tb14958.x
出版商:Blackwell Publishing Ltd
年代:1966
数据来源: WILEY
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| 3. |
Preface |
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Acta Pædiatrica,
Volume 55,
Issue 1,
1966,
Page 5-5
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ISSN:0803-5253
DOI:10.1111/j.1651-2227.1966.tb14959.x
出版商:Blackwell Publishing Ltd
年代:1966
数据来源: WILEY
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| 4. |
Choice of method |
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Acta Pædiatrica,
Volume 55,
Issue 1,
1966,
Page 6-10
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ISSN:0803-5253
DOI:10.1111/j.1651-2227.1966.tb05172.x
出版商:Blackwell Publishing Ltd
年代:1966
数据来源: WILEY
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| 5. |
Introduction |
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Acta Pædiatrica,
Volume 55,
Issue 1,
1966,
Page 7-10
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ISSN:0803-5253
DOI:10.1111/j.1651-2227.1966.tb18048.x
出版商:Blackwell Publishing Ltd
年代:1966
数据来源: WILEY
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| 6. |
BOWEL FUNCTION—A BRIEF REVIEW |
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Acta Pædiatrica,
Volume 55,
Issue 1,
1966,
Page 9-16
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ISSN:0803-5253
DOI:10.1111/j.1651-2227.1966.tb09051.x
出版商:Blackwell Publishing Ltd
年代:1966
数据来源: WILEY
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| 7. |
PURPOSES OF THE STUDY |
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Acta Pædiatrica,
Volume 55,
Issue 1,
1966,
Page 10-10
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ISSN:0803-5253
DOI:10.1111/j.1651-2227.1966.tb09061.x
出版商:Blackwell Publishing Ltd
年代:1966
数据来源: WILEY
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| 8. |
Definitions |
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Acta Pædiatrica,
Volume 55,
Issue 1,
1966,
Page 11-13
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ISSN:0803-5253
DOI:10.1111/j.1651-2227.1966.tb18049.x
出版商:Blackwell Publishing Ltd
年代:1966
数据来源: WILEY
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| 9. |
II: Clinical Material and Methods |
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Acta Pædiatrica,
Volume 55,
Issue 1,
1966,
Page 13-23
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ISSN:0803-5253
DOI:10.1111/j.1651-2227.1966.tb09044.x
出版商:Blackwell Publishing Ltd
年代:1966
数据来源: WILEY
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| 10. |
Material and Methods |
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Acta Pædiatrica,
Volume 55,
Issue 1,
1966,
Page 14-20
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ISSN:0803-5253
DOI:10.1111/j.1651-2227.1966.tb18050.x
出版商:Blackwell Publishing Ltd
年代:1966
数据来源: WILEY
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