摘要:

Abstract:We conducted a prospective study of 20 patients with pig. menting pityriasis alba (PPA) over a period of two years. Characteristic morphology revealed a central zone of bluish hyperpigmentation surrounded by a hypopigmented, slightly scaly halo of variable width. All patients displayed lesions on the face. Concomitant extrafacial Involvement was uncommon. A significant finding was an associated dermatophyte infection in 13 patients (65%). These patients all received griseoful‐vin 10 mg/kg/day for eight weeks, resulting In the resolution of PPA in seven within 4 to 20 weeks. These were also treated with 1% hydrocortt‐sone. Biopsy specimens from two patients showed similar features, namely, a subacute dermatitis with variable pigment Incontinence, lmmu‐nohistochemical labeling revealed a preponderance of T lymphocytes. Pigmenting pityrlasis alba seems to be a variant of classic pityriasis alba showing a strong association with dermatophyte infection, especially tines capitls. It may be related to Iichenoid melanoderma

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1993.tb00001.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY

摘要:

Abstract:Cutis marmorata telanglectatlca congenlta is an uncommon, generally congenital, cutaneous condition. The major skin findings are persistent, fixed cutts marmorata, telangiectasia, and phlebectasia; often, there is associated skin atrophy and ulceratton as well. Significantly, two‐thirds of patients have other congenital anomalles, although often minor ones. We report a series of eight children with cutis marmorata tefangiectatica congenlta, including one with associated congenital hypothyroidism, a relationship that has never before been note

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1993.tb00002.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY

摘要:

Abstract:A 4‐month‐old girl had an isolated, reddish brown nodule on her back that blistered repeatedly. Toluidine blue staining of a biopsy specimen showed a dense infiltration of mast ceils in the upper dermis. In addition, large granules that stained similarly to the normal mast cell granules were observed. Electron microscopic studies disclosed that these giant granules (2–4 pm diameter) had the characteristic substructures of mast cell granules, that is, lamellar and scroll‐like forms. Some giant mast cell granules lost their electron density, suggesting a degran‐utatton process. Aggregates of normal‐size granules with varying degrees of electron density were also observed. We assume that trie variations in morphology of these giant granules represent their maturat

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1993.tb00003.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY

摘要:

Abstract:Cutaneous depressions, commonly known as dimples, are uncommon In locations other than the face. An Infant had deep dimple like depressions near the acromion bilaterally. This most likely represents benign autosomal acromial dimples, a rarely reported autosomal dominant condition. Other causes of dimples include a variety of congenital malformation syndromes, and Infectious, metaboiic, and traumatic etiologies. Awareness of the etiology and significance of skin dimples is helpful to the clinician when confronted with this unusual finding.

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1993.tb00004.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY

摘要:

Abstract:An 8‐year‐old girl had pseudoxanthoma elesticum (PXE) with the characteristic skin and ocular findings. She had no associated systemic symptoms and no family history of PXE. The disease was most likely Inherited In an autosomal recessive fashion. It is reviewed with regard to etiology, Inheritance, diagnosis, and, particularly, manage

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1993.tb00005.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY

摘要:

Abstract:Three sibs were affected by numerous accessory tragi. On clinical examination, no other associated developmental defects, such as the Goldenhar syndrome, were detected.

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1993.tb00006.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY

摘要:

Abstract:The combination of rapid, diffuse alopecia, and neurologic and gastrointestinal disturbance is pathognomonic for thallium toxicity. The hair mount, showing a tapered or bayonet anagen hair with black pigmentation at the base, may be highly diagnostic before the onset of alopecia. We saw a 10‐year‐old boy who suffered from thallium poison

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1993.tb00007.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY

摘要:

Abstract:Postoperative alopecia is an uncommon complication of surgery and is reported mainly in adults who undergo prolonged anesthesia. The disorder occurred In three infants after cardiac surgery. It is easily prevented by frequently changing the position of the head during surgery and the recovery period.

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1993.tb00008.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY

摘要:

Abstract:Two infant boys developed scrotal hairs within the first three months of life. There was no other clinical or biochemical evidence of excessive androgen production, and no further progression of hair growth.

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1993.tb00009.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY

摘要:

Abstract:Although nail abnormalities have been reported to occur in 1% to 10% of patients with lichen planus, in children with lichen planus they are rarely mentioned in the literature. An 11‐year‐old boy had a two‐month history of naii dystrophy affecting all the fingernails and the great toenaiis. The naii plates showed longitudinal ridging and thinning as well as onycholysis and distal splitting. There were no cutaneous or mucous membrane abnormalities. A nail biopsy specimen showed hyperkeratosis, hypergranulosis, and acanthosis in the ventral portion of the proximal nail fold and in the nail matrix. A bandlike lymphocytic infiltrate was present in the superficial dermis, and the basal iayer showed vacuolar alterations. A diagnosis of iichen planus was made. Treatment was intramuscular triamcinolone 20 mg once a month for six months. Since 1969 only 13 proved pediatric cases of lichen planus limited to the nails have been reported, including two children with 20‐nall dystrophy and four with idiopathic atrophy of th

ISSN:0736-8046    

DOI:10.1111/j.1525-1470.1993.tb00010.x

出版商:Blackwell Publishing Ltd    

年代:1993

数据来源: WILEY