AbstractReport of a case, initially diagnosed as Anorexia Nervosa (AN) but later on revealing a fourth Ventricular Tumor is presented. Relevant literature is surveyed while drawing attention to the unusual location of the tumor, instead of hypothalamic area as customarily reported. Several years of duration between initial appearance of clinical signs and symptoms and discovery of the tumor require emphasizing the need to keep the diagnosis tentative and not to hesitate in following up any clues pointing to a probable organic base.