We report the clinical symptoms and the course of a case that showed the typical findings of a meningioma of the optic nerve sheath, characterized by visual disturbances, progressive visual field defect, proptosis, secondary atrophy of the optic disc, and shunt vessels between retinal and choroidal circulation. The shunt vessel which was demonstrated in this case by fluorescein angiography is identical with the optociliary vein reported in the literature. Fluorograms also revealed peculiar vessels at the margin of the optic disc, which have not been described in association with this tumor. CT scanning and roentgenograms of the optic canal proved useful as diagnostic tools for this tumor. The tumor was removed through a frontotemporal craniotomy, preserving the optic nerve. The histopathological diagnosis was meningothelial meningioma.