Clinical Aspects of Bilateral Renal Dysplasia in Children
作者:
Ayfer Gur,
Norman J. Siegel,
Charles A. Davis,
Michael Kashgarian,
John P. Hayslett,
期刊:
Nephron
(Karger Available online 1975)
卷期:
Volume 15,
issue 1
页码: 50-61
ISSN:1660-8151
年代: 1975
DOI:10.1159/000180492
出版商: S. Karger AG
关键词: Dysplasia;Laurence-Moon-Biedl syndrome;Renal insufficiency
数据来源: Karger
摘要:
Despite recent attempts to improve classification and to provide data on pathogenic mechanisms, there is a paucity of information concerning the clinical aspects of bilateral renal dysplasia. Therefore, the clinical features and long-term prognosis of eight patients with bilateral renal dysplasia have been evaluated. Three important observations were made, namely (1) a large proportion of patients had an impairment of urinary concentration and acidification, (2) the clinical course was characterized by progressive renal deterioration in patients with bilateral involvement, and (3) four children with renal dysplasia had the clinical features of Laurence-Moon-Biedl syndrome.
点击下载:
PDF
(1274KB)
返 回