Clinical Picture and Problems of Keratoplasty in Richner-Hanhart Syndrome (Tyrosinemia Type II)
作者:
R.B. Sayar,
D. von Domarus,
H.-J. Schäfer,
G. Beckenkamp,
期刊:
Ophthalmologica
(Karger Available online 1988)
卷期:
Volume 197,
issue 1
页码: 1-6
ISSN:0030-3755
年代: 1988
DOI:10.1159/000309909
出版商: S. Karger AG
关键词: Richner-Hanhart syndrome;Tyrosinemia type II;Metabolic disease
数据来源: Karger
摘要:
The Richner-Hanhart syndrome seen in a middle-aged woman is described. The patient had the typical clinical manifestations of tyrosinemia II with a bilateral keratopathy, palmar and plantar hyperkeratosis. The patient was subjected to a specific diet and to perforating keratoplasty. Postoperative systemic therapy with steroids had a negative influence on the clinical manifestations; dendritic lesions which developed on the corneal graft disappeared after interruption of the systemic steroid therapy. This suggests that cortisone treatment after keratoplasty should be avoided in this special metabolic disorder.
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